Comments on the article “Clinical application of Nuss procedure for chest wall deformity in Poland syndrome”
نویسنده
چکیده
Poland’s syndrome is a very rare type of chest deformation found in 1 : 32,000 – 1 : 52,500 live births [1, 2]. Its treatment most often involves the reconstruction of the mammary glands with the transposition of a pedicled muscle-skin flap using Marlex mesh [3, 4] or the repair of the chest’s bone structure. The coexistence of multiple developmental defects of the chest constituting this syndrome and the asymmetric character of the deformation increase the difficulty of performing a successful correction. The authors of the present study describe a method of treating Poland’s syndrome, employed in a 4-year-old female patient, using the minimally invasive Nuss method as the first stage of treatment, preparing the conditions for a final correction during puberty. However, performing the Nuss procedure on a 4-year-old asymptomatic child raises some questions. Although some authors believe that the Nuss procedure should be performed as early as possible, provided that the patient is at least 3 years old [5, 6], and that the method is safe and not burdened with a high rate of complications, achieving a satisfactory effect of correction in these Poland’s syndrome patients is very challenging, as indicated by this report as well as others [7]. It appears that performing a single repair procedure that combines elements of the Ravitch method and the Nuss method during puberty, and, perhaps, supplementing it with mammary gland reconstruction, would improve not only internal, but especially external correction. I also do not share the concern of the authors pertaining to the complications which can occur in classic plastic repair of the anterior thoracic wall. Complex correction of developmental thoracic defects should be selected as the treatment of choice in the case of large asymmetric deformations for which the Nuss method alone is insufficient. The complications occurring as a result of the two treatment methods are comparable.
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First Iranian Experience of the Minimally Invasive Nuss Procedure for Pectus Excavatum Repair: A Case Series and Literature Review
Pectus excavatum is the most common congenital deformity of the chest wall. The most frequently used techniques include Ravitch (costochondral resection) and Nuss (minimally invasive pectus repair of pectus excavatum [MIRPE]). The Nuss technique includes using temporary metallic bars without costochondral resection to correct the chest wall deformity. Modified MIRPE can be learned easily and pe...
متن کاملClinical application of Nuss procedure for chest wall deformity in Poland syndrome
A 6-year-old girl with Poland syndrome was diagnosed with loss of hard and soft tissue on her affected chest. She required chest reconstruction to protect her thorax and improve her developmental delay. We applied a titanium device used for children with funnel chest to her, resulting in good shape. By using this device, we avoided sacrificing healthy rib and muscle; she could save the tissue f...
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Background: Infants and children present with a wide range of congenital chest wall deformities which have both physiologic psychologic consequences and are often associated with other abnormalities. Surgical intervention offers excellent cosmetic results with minimal morbidity and mortality. In order to investigation of chest wall deformities, and surgical results, this study was performed. M...
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OBJECTIVE In 1998, Dr Donald Nuss proposed minimally invasive repair of pectus excavatum (MIRPE) which did not require the osteochondrous parts of the anterior chest wall to be resected. The paper aims at presenting the authors' own 6 years of experience in funnel chest repair with MIRPE technique. Also, many technical problems of this method are discussed. MATERIALS AND METHODS Between 1999 ...
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Pectus excavatum is a deformity of the thoracic wall present in less than 1% of the population. Treatment is essentially surgical because of the size of the deformity. The most employed surgical options are the technique proposed by Ravitch and its variations and the technique proposed by Nuss. The first one is considered the conventional technique, while the Nuss procedure is minimally invasiv...
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